{"id":167,"date":"2018-10-12T12:25:14","date_gmt":"2018-10-12T11:25:14","guid":{"rendered":"https:\/\/research.reading.ac.uk\/neurodegenerative-diseases\/?page_id=167"},"modified":"2021-01-04T12:20:47","modified_gmt":"2021-01-04T12:20:47","slug":"huntingtons-disease","status":"publish","type":"page","link":"https:\/\/research.reading.ac.uk\/neurodegenerative-diseases\/huntingtons-disease\/","title":{"rendered":"Huntington&#8217;s disease"},"content":{"rendered":"<p><span style=\"color: #0000ff\"><strong>Huntington&#8217;s disease health-related quality of life questionnair<\/strong><\/span><strong style=\"letter-spacing: 0.08px;color: #0000ff\">e (HDQoL)<\/strong><\/p>\n<p><a href=\"https:\/\/research.reading.ac.uk\/neurodegenerative-diseases\/hdqol\/\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft wp-image-152 \" style=\"letter-spacing: 0.08px\" src=\"https:\/\/research.reading.ac.uk\/neurodegenerative-diseases\/wp-content\/uploads\/sites\/65\/logos\/hdqol-logo.png\" alt=\"\" width=\"168\" height=\"168\" \/><\/a><\/p>\n<p>&nbsp;<\/p>\n<p>&nbsp;<\/p>\n<p>&nbsp;<\/p>\n<p>&nbsp;<\/p>\n<p><a href=\"http:\/\/www.carehd.eu\/\"><span style=\"color: #0000ff\"><strong>Care-HD Horizon 2020 research programme<\/strong><\/span><\/a><\/p>\n<p><span style=\"color: #0000ff\"><strong><img loading=\"lazy\" decoding=\"async\" class=\"alignnone  wp-image-656\" src=\"https:\/\/research.reading.ac.uk\/neurodegenerative-diseases\/wp-content\/uploads\/sites\/65\/2021\/01\/CareHDlogo-300x122.jpg\" alt=\"\" width=\"270\" height=\"110\" srcset=\"https:\/\/research.reading.ac.uk\/neurodegenerative-diseases\/wp-content\/uploads\/sites\/65\/2021\/01\/CareHDlogo-300x122.jpg 300w, https:\/\/research.reading.ac.uk\/neurodegenerative-diseases\/wp-content\/uploads\/sites\/65\/2021\/01\/CareHDlogo.jpg 547w\" sizes=\"auto, (max-width: 270px) 100vw, 270px\" \/><\/strong><\/span><\/p>\n<p><span style=\"color: #0000ff\"><strong>Publications<\/strong><\/span><\/p>\n<p><strong>Ho AK.<\/strong> (2019).<strong><a href=\"https:\/\/books.google.co.uk\/books?hl=en&amp;lr=&amp;id=kQWSDwAAQBAJ&amp;oi=fnd&amp;pg=PA88&amp;ots=4sJHa0Y2r7&amp;sig=eHN6-E9Ogytexwev6ipCt0lN2u0#v=onepage&amp;q&amp;f=false\"> Huntington\u2019s disease<\/a><\/strong>. In Degenerative Disorders of the Brain (pp. 88-115). Routledge.<\/p>\n<p>Aubeeluck AV, Stupple EJ, Schofield M, Hughes A, Van der Meer L, Landwehrmeyer GB, &amp; <strong>Ho AK.<\/strong> (2019).<strong><a href=\"http:\/\/centaur.reading.ac.uk\/84656\/\"> An International validation of a clinical tool to assess carers\u2019 quality of life in Huntington\u2019s Disease<\/a>.<\/strong> Frontiers in Psychology, 10, 1658.<\/p>\n<p>Maxan A, Mason S, Saint\u2010Pierre M, Smith E, <strong>Ho AK<\/strong>, Harrower T, Watts C, Tai Y, Pavese N, Savage JC &amp; Tremblay M\u00c8. (2018).<strong> <a href=\"https:\/\/onlinelibrary.wiley.com\/doi\/full\/10.1002\/ana.25354\">Outcome of cell suspension allografts in a patient with Huntington&#8217;s disease<\/a>.<\/strong> Annals of Neurology, 84(6), pp.950-956.<\/p>\n<p>Mestre TA, Busse M, Davis AM, Quinn L, Rodrigues FB, Burgunder JM, Carlozzi NE, Walker F, <strong>Ho AK<\/strong>, Sampaio C. &amp; Goetz CG. (2018). <a href=\"http:\/\/centaur.reading.ac.uk\/75096\/\"><strong>Rating scales and performance\u2010based measures for assessment of functional ability in Huntington&#8217;s disease: critique and recommendations<\/strong><\/a>. Movement Disorders Clinical Practice, 5(4), pp.361-372.<\/p>\n<p>Barker RA, Mason SL, Harrower TP, Swain RA, <strong>Ho AK<\/strong>, Sahakian BJ, Mathur R, Elneil S, Thornton S, Hurrelbrink C. &amp; Armstrong RJ. (2013). <a href=\"http:\/\/centaur.reading.ac.uk\/32446\/\"><strong>The long-term safety and efficacy of bilateral transplantation of human fetal striatal tissue in patients with mild to moderate Huntington&#8217;s disease<\/strong><\/a>. Journal of Neurology, Neurosurgery &amp; Psychiatry, 84(6), pp.657-665.<\/p>\n<p>Vaccarino AL, Sills T, Anderson KE, Borowsky B, Craufurd D, Giuliano J, Goodman L, Guttman M, Kupchak P, <strong>Ho AK<\/strong>, Paulsen JS, C Stout J, van Kammen DP, Evans K. (2011). <a href=\"http:\/\/centaur.reading.ac.uk\/26356\/\"><strong>Assessment of Cognitive Symptoms in Prodromal and Early Huntington Disease<\/strong><\/a>. PLoS Curr, Oct 25;3:RRN1250.<\/p>\n<p>Vaccarino AL, Sills T, Anderson KE, Endicott J, Giuliano J, Guttman M, <strong>Ho AK<\/strong>, Kupchak P, Paulsen JS, Warner JH, Williams J, Evans K. (2011). <a href=\"http:\/\/centaur.reading.ac.uk\/26357\/\"><strong>Assessment of Day-to-Day Functioning in Prodromal and Early Huntington Disease.<\/strong><\/a> PLoS Curr, Sep 12;3:RRN1262.<\/p>\n<p><strong>Ho AK<\/strong>, Hocaoglu MB; European Huntington&#8217;s Disease Network Quality of Life Working Group. (2011). <a href=\"http:\/\/centaur.reading.ac.uk\/26367\/\"><strong>Impact of Huntington&#8217;s across the entire disease spectrum: the phases and stages of disease from the patient perspective<\/strong><\/a>. Clinical Genetics, Sep;80(3):235-9.<\/p>\n<p>Vaccarino AL, Anderson KE, Borowsky B, Coccaro E, Craufurd D, Endicott J, Giuliano J, Groves M, Guttman M, <strong>Ho AK<\/strong>, Kupchak P, Paulsen JS, Stanford MS, van Kammen DP, Watson D, Wu KD, Evans K. (2011). <strong><a href=\"http:\/\/centaur.reading.ac.uk\/26359\/\">Assessing Behavioural Manifestations Prior to Clinical Diagnosis of Huntington Disease: &#8220;Anger and Irritability&#8221; and &#8220;Obsessions and Compulsions&#8221;<\/a><\/strong>. PLoS Curr, Jul 11;3:RRN1241.<\/p>\n<p>Vaccarino AL, Sills T, Anderson KE, Bachoud-L\u00e9vi AC, Borowsky B, Craufurd D, Duff K, Giuliano J, Groves M, Guttman M, Kupchak P, <strong>Ho AK<\/strong>, Paulsen JS, Pedersen KF, van Duijn E, van Kammen DP, Evans K. (2011). <a href=\"http:\/\/centaur.reading.ac.uk\/26360\/\"><strong>Assessment of Depression, Anxiety and Apathy in Prodromal and Early Huntington Disease.<\/strong><\/a> PLoS Curr, Jun 17;3:RRN1242.<\/p>\n<p>Vaccarino AL, Sills T, Anderson KE, Biglan K, Borowsky B, Giuliano J, Guttman M, <strong>Ho AK<\/strong>, Kennard C, Kupchak P, Landwehrmeyer GB, Michell A, Paulsen JS, Reilmann R, van Kammen DP, Warner JH, Evans K. (2011). <a href=\"http:\/\/centaur.reading.ac.uk\/26361\/\"><strong>Assessment of Motor Symptoms and Functional Impact in Prodromal and Early Huntington Disease.<\/strong><\/a> PLoS Curr, Jun 14;2:RRN1244.<\/p>\n<p>Vaccarino AL, Anderson K, Borowsky B, Duff K, Giuliano J, Guttman M, <strong>Ho AK<\/strong>, Orth M, Paulsen JS, Sills T, van Kammen DP, Evans KR; PREDICT-HD and REGISTRY Investigators Coordinators. (2011). <a href=\"http:\/\/centaur.reading.ac.uk\/26362\/\"><strong>An item response analysis of the motor and behavioural subscales of the unified Huntington&#8217;s disease rating scale in huntington disease gene expansion carriers<\/strong><\/a>. Movement Disorders, Apr;26(5):877-84.<\/p>\n<p>Orth M, Handley OJ, Schwenke C, Dunnett SB, Craufurd D, <strong>Ho AK<\/strong>, Wild E, Tabrizi SJ, Landwehrmeyer GB; Investigators of the European Huntington&#8217;s Disease Network. (2010). <strong><a href=\"http:\/\/centaur.reading.ac.uk\/26363\/\">Observing Huntington&#8217;s Disease: the European Huntington&#8217;s Disease Network&#8217;s REGISTRY<\/a><\/strong>. PLoS Curr, Sep 28;2.<\/p>\n<p>Mason SL, Wijeyekoon R, Swain R, <strong>Ho AK<\/strong>, Smith EL, Sahakian B, Barker RA. (2010). <strong><a href=\"http:\/\/centaur.reading.ac.uk\/26364\/\">Cognitive follow up of a small cohort of Huntington&#8217;s disease patients over a 5 year period<\/a>.<\/strong> PLoS Curr, Sep 7;2. pii: RRN1174.<\/p>\n<p>Robbins AO, <strong>Ho, AK<\/strong>, Barker RA. (2006). <a href=\"https:\/\/onlinelibrary.wiley.com\/doi\/full\/10.1111\/j.1468-1331.2006.01319.x\"><strong>Weight changes in Huntington&#8217;s disease<\/strong><\/a>. European Journal of Neurology,\u00a0 Aug;13(8):e7.<\/p>\n<p>Pavese N, Gerhard A, Tai YF, <strong>Ho, AK<\/strong>, Turkheimer F, Barker RA, Brooks DJ, Piccini P. (2006). <a href=\"http:\/\/centaur.reading.ac.uk\/13899\/\"><strong>Microglial activation correlates with severity in Huntington disease: a clinical and PET study. Neurology<\/strong><\/a>, Jun 13;66(11):1638-43.<\/p>\n<p><strong>Ho, AK<\/strong>, Robbins AO, Barker RA. (2006). <a href=\"http:\/\/centaur.reading.ac.uk\/14012\/\"><strong>Huntington&#8217;s disease patients have selective problems with insight<\/strong><\/a>. Movement Disorders, Mar;21(3):385-9. PubMed PMID: 16211608.<\/p>\n<p><strong>Ho, AK<\/strong>, Sahakian BJ, Robbins TW, Barker RA. (2004). <a href=\"https:\/\/journals.lww.com\/cogbehavneurol\/Abstract\/2004\/12000\/Random_Number_Generation_in_Patients_with.5.aspx\"><strong>Random number generation in patients with symptomatic and presymptomatic Huntington&#8217;s disease<\/strong><\/a>. Cognitive and Behavioural Neurology, Dec;17(4):208-12.<\/p>\n<p><strong>Ho, AK<\/strong>, Nestor PJ, Williams GB, Bradshaw JL, Sahakian BJ, Robbins TW, Barker RA. (2004).<a href=\"http:\/\/centaur.reading.ac.uk\/14013\/\"><strong> Pseudo-neglect in Huntington&#8217;s disease correlates with decreased angular gyrus density.<\/strong> <\/a>Neuroreport, Apr 29;15(6):1061-4.<\/p>\n<p><strong>Ho, AK<\/strong>, Sahakian BJ, Brown RG, Barker RA, Hodges JR, An\u00e9 MN, Snowden J, Thompson J, Esmonde T, Gentry R, Moore JW, Bodner T; NEST-HD Consortium. (2003). <a href=\"https:\/\/n.neurology.org\/content\/61\/12\/1702.short\"><strong>Profile of cognitive progression in early Huntington&#8217;s disease<\/strong><\/a>. Neurology, Dec 23;61(12):1702-6.<\/p>\n<p><strong>Ho, AK<\/strong>, Manly T, Nestor PJ, Sahakian BJ, Bak TH, Robbins TW, Rosser AE, Barker RA. (2003). <a href=\"https:\/\/www.tandfonline.com\/doi\/abs\/10.1076\/neur.9.3.261.15559\"><strong>A case of unilateral neglect in Huntington&#8217;s disease<\/strong><\/a>. Neurocase, Jun;9(3):261-73.<\/p>\n<p>Pavese N, Andrews TC, Brooks DJ, <strong>Ho AK<\/strong>, Rosser AE, Barker RA, Robbins TW, Sahakian BJ, Dunnett SB, Piccini P. (2003). <a href=\"https:\/\/academic.oup.com\/brain\/article\/126\/5\/1127\/489359?login=true\"><strong>Progressive striatal and cortical dopamine receptor dysfunction in Huntington&#8217;s disease: a PET study<\/strong><\/a>. Brain, May;126(Pt 5):1127-35.<\/p>\n<p>Rosser AE, Barker RA, Harrower T, Watts C, Farrington M, <strong>Ho, AK<\/strong>, Burnstein RM, Menon DK, Gillard JH, Pickard J, Dunnett SB; NEST-UK. (2002). <a href=\"https:\/\/jnnp.bmj.com\/content\/73\/6\/678.short\"><strong>Unilateral transplantation of human primary fetal tissue in four patients with Huntington&#8217;s disease: NEST-UK safety report ISRCTN no 36485475<\/strong><\/a>. Journal of Neurology Neurosurgery and Psychiatry, Dec;73(6):678-85.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Huntington&#8217;s disease health-related quality of life questionnaire (HDQoL) &nbsp; &nbsp; &nbsp; &nbsp; Care-HD Horizon 2020 research programme Publications Ho AK. (2019). Huntington\u2019s disease. In Degenerative Disorders of the Brain (pp&#8230;.<a class=\"read-more\" href=\"&#104;&#116;&#116;&#112;&#115;&#58;&#47;&#47;&#114;&#101;&#115;&#101;&#97;&#114;&#99;&#104;&#46;&#114;&#101;&#97;&#100;&#105;&#110;&#103;&#46;&#97;&#99;&#46;&#117;&#107;&#47;&#110;&#101;&#117;&#114;&#111;&#100;&#101;&#103;&#101;&#110;&#101;&#114;&#97;&#116;&#105;&#118;&#101;&#45;&#100;&#105;&#115;&#101;&#97;&#115;&#101;&#115;&#47;&#104;&#117;&#110;&#116;&#105;&#110;&#103;&#116;&#111;&#110;&#115;&#45;&#100;&#105;&#115;&#101;&#97;&#115;&#101;&#47;\">Read More ><\/a><\/p>\n","protected":false},"author":111,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"__cvm_playback_settings":[],"__cvm_video_id":"","footnotes":""},"class_list":["post-167","page","type-page","status-publish","hentry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v21.8.1 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Huntington&#039;s disease - Neuro Projects<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/research.reading.ac.uk\/neurodegenerative-diseases\/huntingtons-disease\/\" \/>\n<meta property=\"og:locale\" content=\"en_GB\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Huntington&#039;s disease - Neuro Projects\" \/>\n<meta property=\"og:description\" content=\"Huntington&#8217;s disease health-related quality of life questionnaire (HDQoL) &nbsp; &nbsp; &nbsp; &nbsp; Care-HD Horizon 2020 research programme Publications Ho AK. 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